Affiliation:
1. Chita State Medical Academy
2. Regional Children's Clinical Hospital
Abstract
Every pediatrician-nephrologist repeatedly have to deal with cases of the birth of childrenwith early onset of nephrotic syndrome, which is characterized by a severe course, persistent progression ofsymptoms, resistance to standard immunosuppressive therapy, questionable and, often, unfavorable prognosesfor life and health, which requires constant improvement of existing professional knowledge, diagnostic andtherapeutic skills. The article presents a review of the scientific literature of domestic and foreign authors,which allows changing the perception of the disease, improving outcomes, giving chances to the patient andhis family in conditions of modern and timely diagnosis and the correct choice of patient management strategy.
Publisher
Chita State Medical Academy
Reference17 articles.
1. Detskaya nefrologiya : uchebnik / pod red. P.V. SHumilova, E.K. Petrosyan, O.L. CHugunovoj. – M. : MEDpress-inform, 2021. – 616 s. : il.
2. Boyer O. Management of congenital nephrotic syndrome: consensus recommendations of the ERKNetESPN Working Group / O. Boyer, F. Schaefer, D. Haffner, D. Bockenhauer [et al.] // Nat Rev Nephrol. 2021 Apr; 17 (4): 277–289. doi: 10.1038/s41581-020-00384-1.
3. Noone D. K. Idiopathic nephrotic syndrome in children / D.G. Noone, K. Iijima, R. Parekh // Lancet. 2018. – Jul 7;392 (10141): 61–74. doi: 10.1016/S0140-6736(18)30536-1.
4. Kemper M.J. Difficult-to-treat idiopathic nephrotic syndrome: established drugs, open questions and future options / M.J. Kemper, L. Valentin, M. Husen // Pediatr Nephrol. 2018. – Oct; 33( 10): 1641–1649. doi: 10.1007/s00467-017-3780-7.
5. Bataeva E.P., Baldynyuk O.V., Kazanceva A.N., Zameshaev M.S., Molchanova T.S., Kalinina L.R., Zeleneva A.YU. Redkij sluchaj nasledstvennogo vrozhdennogo infantil'nogo nefroticheskogo sindroma u novorozhdennogo rebenka Zabajkal'skij medicinskij zhurnal. 4. 2022 . 27–32.