Anesthetic Management of a Patient with Poland’s syndrome: A Case Report

Abstract

Poland syndrome is a rare congenital disease characterized by various degrees of chest wall defects, such as deficits in the small thoracic muscle and defects in the neuromuscular region of the small thoracic muscle. In addition, this condition may present with loss or weak development of the papilla and breasts and can be accompanied by brachydactyly, syndactyly, and limb defects in the hands and feet on the same side. Poland syndrome also may cause various deformities in the heart, lungs, and kidneys. These lung deformities can produce hypoventilation and hypoxia as the function of the respiratory muscle decreases, leading to increased pulmonary complications postoperatively. Since these patients also have an increased risk of malignant hyperthermia, careful attention is required in the selection of drugs for inducing general anesthesia. We would like to report an experience of general anesthesia for breast reconstruction in a 20-year-old female patient with Poland syndrome.