Discovery of Clinically Approved Agents That Promote Suppression of Cystic Fibrosis Transmembrane Conductance Regulator Nonsense Mutations-Reference-Cited by-同舟云学术

Discovery of Clinically Approved Agents That Promote Suppression of Cystic Fibrosis Transmembrane Conductance Regulator Nonsense Mutations

Published:2016-11 Issue:9 Volume:194 Page:1092-1103
ISSN:1073-449X
Container-title:American Journal of Respiratory and Critical Care Medicine
language:en
Short-container-title:Am J Respir Crit Care Med

Author:

Mutyam Venkateshwar,Du Ming,Xue Xiaojiao,Keeling Kim M.,White E. Lucile,Bostwick J. Robert,Rasmussen Lynn,Liu Bo,Mazur Marina,Hong Jeong S.,Falk Libby Emily,Liang Feng,Shang Haibo,Mense Martin,Suto Mark J.,Bedwell David M.,Rowe Steven M.^ORCID

Publisher

American Thoracic Society

Subject

Critical Care and Intensive Care Medicine,Pulmonary and Respiratory Medicine

Reference41 articles.

1. Cystic Fibrosis

2. Molecular mechanisms of CFTR chloride channel dysfunction in cystic fibrosis

3. Cystic fibrosis transmembrane conductance regulator protein repair as a therapeutic strategy in cystic fibrosis

4. Suppression of premature termination codons as a therapeutic approach

5. Gentamicin-mediated suppression of Hurler syndrome stop mutations restores a low level of alpha-L-iduronidase activity and reduces lysosomal glycosaminoglycan accumulation

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