The Biological Effects of Double-Dose Alpha-1 Antitrypsin Augmentation Therapy. A Pilot Clinical Trial-Reference-Cited by-同舟云学术

The Biological Effects of Double-Dose Alpha-1 Antitrypsin Augmentation Therapy. A Pilot Clinical Trial

Published:2019-08 Issue:3 Volume:200 Page:318-326
ISSN:1073-449X
Container-title:American Journal of Respiratory and Critical Care Medicine
language:en
Short-container-title:Am J Respir Crit Care Med

Author:

Campos Michael A.¹^ORCID,Geraghty Patrick²^ORCID,Holt Gregory¹,Mendes Eliana¹,Newby Paul R.³,Ma Shuren⁴,Luna-Diaz Landy V.⁵,Turino Gerard M.⁴,Stockley Robert A.⁶

Affiliation:

1. Division of Pulmonary, Allergy, Critical Care and Sleep Medicine, University of Miami School of Medicine, Miami, Florida

2. Department of Medicine and Cell Biology, State University of New York Downstate Medical Center, Brooklyn, New York

3. University of Birmingham, Birmingham, United Kingdom

4. Mount Sinai Icahn School of Medicine, New York, New York

5. Jackson Memorial Hospital, Miami, Florida; and

6. Lung Investigation Unit, Queen Elizabeth Hospital, Birmingham, United Kingdom

Publisher

American Thoracic Society

Subject

Critical Care and Intensive Care Medicine,Pulmonary and Respiratory Medicine

Link

https://www.atsjournals.org/doi/pdf/10.1164/rccm.201901-0010OC

Reference59 articles.

1. A Review of α1-Antitrypsin Deficiency

2. Unopposed Cathepsin G, Neutrophil Elastase, and Proteinase 3 Cause Severe Lung Damage and Emphysema

3. The discovery of α1-antitrypsin and its role in health and disease

4. Lung lavage fluid from patients with α1-proteinase inhibitor deficiency or chronic obstructive bronchitis: anti-elastase function and cell profile

5. Bronchial Inflammation

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