Cyclodextrin overcomes the transport defect in nearly every organ of NPC1 mice leading to excretion of sequestered cholesterol as bile acid
Author:
Publisher
Elsevier BV
Subject
Cell Biology,Endocrinology,Biochemistry
Reference46 articles.
1. Niemann-Pick disease type C: a cellular cholesterol lipidosis;Pentchev,1995
2. A riddle wrapped in a mystery: understanding Niemann-Pick disease, type C;Patterson;Neurologist.,2003
3. Niemann-Pick disease type C;Vanier;Clin. Genet.,2003
4. Ultrastructural changes in the lung in Niemann-Pick type C mouse;Manabe;Virchows Arch.,1995
5. The Niemann-Pick C1 protein resides in a vesicular compartment linked to retrograde transport of multiple lysosomal cargo;Neufeld;J. Biol. Chem.,1999
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