L'hérédo-dystrophie mouchetée du parenchyme cornéen

Abstract

SUMMARYThe authors describe a new hereditary dystrophy of the cornea, the specked heredo-dystrophy of the corneal parenchyma. In the corneal stroma of both eyes speckles can be easily distinguished; they are more or less numerous and can be found in all the layers of the parenchyma, as well in the center as at the periphery. Dimension, shape and density of the speckles are very variable: they are oval, round or festooned; some of them are opaque at the borders; others show a more diffuse trouble; others are dotted; their borders are well-cut, regular or indented. In optical section the opacities are thin and flat. This dystrophy is not evolutive and is transmitted as an autosomal regular dominant trait. One member of the affected family shows a cloudy central dystrophy of the corneal stroma, so that it is possible that there exists a relationship between these two affections.