Improvement of Neuromuscular Synaptic Phenotypes without Enhanced Survival and Motor Function in Severe Spinal Muscular Atrophy Mice Selectively Rescued in Motor Neurons
Author:
Publisher
Public Library of Science (PLoS)
Subject
Multidisciplinary
Reference34 articles.
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4. SMNDelta7, the major product of the centromeric survival motor neuron (SMN2) gene, extends survival in mice with spinal muscular atrophy and associates with full-length SMN;TT Le;Hum Mol Genet,2005
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