Deficient and Null Variants of SERPINA1 Are Proteotoxic in a Caenorhabditis elegans Model of α1-Antitrypsin Deficiency-Reference-Cited by-同舟云学术

Deficient and Null Variants of SERPINA1 Are Proteotoxic in a Caenorhabditis elegans Model of α1-Antitrypsin Deficiency

Published:2015-10-29 Issue:10 Volume:10 Page:e0141542
ISSN:1932-6203
Container-title:PLOS ONE
language:en
Short-container-title:PLoS ONE

Author:

Cummings Erin E.,O’Reilly Linda P.,King Dale E.,Silverman Richard M.,Miedel Mark T.,Luke Cliff J.,Perlmutter David H.,Silverman Gary A.,Pak Stephen C.

Publisher

Public Library of Science (PLoS)

Subject

Multidisciplinary

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4. Kinetic mechanism of the inhibition of cathepsin G by alpha 1-antichymotrypsin and alpha 1-proteinase inhibitor;J Duranton;Biochemistry,1998

5. Alpha1-antitrypsin deficiency;JK Stoller;Lancet,2005

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