Mitochondrial Network Genes in the Skeletal Muscle of Amyotrophic Lateral Sclerosis Patients

Author:

Bernardini Camilla,Censi Federica,Lattanzi Wanda,Barba Marta,Calcagnini Giovanni,Giuliani Alessandro,Tasca Giorgio,Sabatelli Mario,Ricci Enzo,Michetti Fabrizio

Publisher

Public Library of Science (PLoS)

Subject

Multidisciplinary

Reference43 articles.

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2. Hind limb muscle atrophy precedes cerebral neuronal degeneration in G93A-SOD1 mouse model of amyotrophic lateral sclerosis: a longitudinal MRI study. Exp Neurol;S Marcuzzo,2011

3. Muscle mitochondrial uncoupling dismantles neuromuscular junction and triggers distal degeneration of motor neurons;L Dupuis;PLoS One,2009

4. Skeletal muscle-restricted expression of human SOD1 causes motor neuron degeneration in transgenic mice;M Wong;Hum Mol Genet,2010

5. Human skeletal muscle atrophy in amyotrophic lateralsclerosis reveals a reduction in Akt and an increase in atrogin-1. FASEB J;B Léger,2006

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