Small Molecules Restore Bestrophin 1 Expression and Function of Both Dominant and Recessive Bestrophinopathies in Patient-Derived Retinal Pigment Epithelium-Reference-Cited by-同舟云学术

Small Molecules Restore Bestrophin 1 Expression and Function of Both Dominant and Recessive Bestrophinopathies in Patient-Derived Retinal Pigment Epithelium

Published:2020-05-18 Issue:5 Volume:61 Page:28
ISSN:1552-5783
Container-title:Investigative Opthalmology & Visual Science
language:en
Short-container-title:Invest. Ophthalmol. Vis. Sci.

Author:

Liu Jingshu¹,Taylor Rachel L.¹,Baines Richard A.²,Swanton Lisa³,Freeman Sally⁴,Corneo Barbara⁵,Patel Achchhe⁵,Marmorstein Alan⁶,Knudsen Travis⁶,Black Graeme C.¹⁷,Manson Forbes¹

Affiliation:

1. Division of Evolution and Genomic Sciences, Faculty of Biology, The University of Manchester, Manchester, United Kingdom

2. Division of Neuroscience and Experimental Psychology, Faculty of Biology, Medicine and Health, The University of Manchester, Manchester, United Kingdom

3. Division of Molecular and Cellular Function, Faculty of Biology, Medicine and Health, The University of Manchester, Manchester, United Kingdom

4. Division of Pharmacy & Optometry, Faculty of Biology, Medicine and Health, The University of Manchester, Manchester, United Kingdom

5. Stem Cell Core Facility, Columbia University Medical Centre, New York, New York, United States

6. Department of Ophthalmology, Mayo Clinic, Rochester, Minnesota, United States

7. Manchester Centre for Genomic Medicine, Manchester Academic Health Sciences Centre, Manchester University NHS Foundation Trust, St Mary's Hospital, Manchester, United Kingdom

Publisher

Association for Research in Vision and Ophthalmology (ARVO)

Subject

General Medicine

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5. Heterogeneity of Potassium Channels in Human Embryonic Stem Cell-Derived Retinal Pigment Epithelium;Stem Cells Translational Medicine;2022-05-27