1. Department of Biochemistry and Molecular Biology, Monash University, Clayton 3800, Victoria, Australia
2. Muscle Development Unit, the Children's Medical Research Institute, Westmead, Sydney 2145, New South Wales, Australia
3. School of Medical Sciences, the University of New South Wales, Sydney 2052, New South Wales, Australia
4. Division of Neurology, the Children's Hospital of Philadelphia, Pennsylvania Muscle Institute, University of Pennsylvania School of Medicine, Philadelphia, PA 19104