Synthetic Aminoglycosides Efficiently Suppress Cystic Fibrosis Transmembrane Conductance Regulator Nonsense Mutations and Are Enhanced by Ivacaftor-Reference-Cited by-同舟云学术

Synthetic Aminoglycosides Efficiently Suppress Cystic Fibrosis Transmembrane Conductance Regulator Nonsense Mutations and Are Enhanced by Ivacaftor

Published:2014-04 Issue:4 Volume:50 Page:805-816
ISSN:1044-1549
Container-title:American Journal of Respiratory Cell and Molecular Biology
language:en
Short-container-title:Am J Respir Cell Mol Biol

Author:

Xue Xiaojiao,Mutyam Venkateshwar,Tang Liping,Biswas Silpak,Du Ming,Jackson Laura A.,Dai Yanying,Belakhov Valery,Shalev Moran,Chen Fuquan,Schacht Jochen,J. Bridges Robert,Baasov Timor,Hong Jeong,Bedwell David M.,Rowe Steven M.

Publisher

American Thoracic Society

Subject

Cell Biology,Clinical Biochemistry,Pulmonary and Respiratory Medicine,Molecular Biology

Reference55 articles.

1. Cystic Fibrosis

2. The Relation between Genotype and Phenotype in Cystic Fibrosis — Analysis of the Most Common Mutation (ΔF508)

3. Suppression of premature termination codons as a therapeutic approach

4. Suppression of a CFTR premature stop mutation in a bronchial epithelial cell line

5. Aminoglycoside antibiotics restore CFTR function by overcoming premature stop mutations

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