4PBA Restores Signaling of a Cysteine-substituted Mutant BMPR2 Receptor Found in Patients with Pulmonary Arterial Hypertension-Reference-Cited by-同舟云学术

4PBA Restores Signaling of a Cysteine-substituted Mutant BMPR2 Receptor Found in Patients with Pulmonary Arterial Hypertension

Published:2020-08 Issue:2 Volume:63 Page:160-171
ISSN:1044-1549
Container-title:American Journal of Respiratory Cell and Molecular Biology
language:en
Short-container-title:Am J Respir Cell Mol Biol

Author:

Dunmore Benjamin J.¹,Yang XuDong¹,Crosby Alexi¹,Moore Stephen¹,Long Lu¹,Huang Christopher¹,Southwood Mark²,Austin Eric D.³,Rana Amer¹^ORCID,Upton Paul D.¹,Morrell Nicholas W.¹^ORCID

Affiliation:

1. Department of Medicine, University of Cambridge School of Clinical Medicine, Addenbrooke’s and Royal Papworth Hospitals, Cambridge, United Kingdom

2. Pathology Research, Royal Papworth Hospital NHS Foundation Trust, Cambridge, United Kingdom; and

3. Department of Pediatrics, Vanderbilt University Medical Center, Nashville, Tennessee

Publisher

American Thoracic Society

Subject

Cell Biology,Clinical Biochemistry,Pulmonary and Respiratory Medicine,Molecular Biology

Reference53 articles.

1. Changing Demographics, Epidemiology, and Survival of Incident Pulmonary Arterial Hypertension

2. Pathology of Pulmonary Hypertension

3. Heterozygous germline mutations in BMPR2, encoding a TGF-β receptor, cause familial primary pulmonary hypertension

4. Familial Primary Pulmonary Hypertension (Gene PPH1) Is Caused by Mutations in the Bone Morphogenetic Protein Receptor–II Gene

5. Genetics and Genomics of Pulmonary Arterial Hypertension

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