A new missense mutation in the BCKDHB gene causes the classic form of maple syrup urine disease (MSUD)

Author:

Miryounesi Mohammad,Ghafouri-Fard Soudeh,Goodarzi Hamedreza,Fardaei Majid

Abstract

AbstractMaple syrup urine disease (MSUD) is an autosomal recessive metabolic disease caused by mutations in the

Publisher

Walter de Gruyter GmbH

Subject

Endocrinology,Endocrinology, Diabetes and Metabolism,Pediatrics, Perinatology and Child Health

Reference12 articles.

1. Maple syrup urine disease : further evidence that newborn screening may fail to identify variant forms;Puckett;Mol Genet Metab,2010

2. Two novel mutations in the BCKDHB gene cause the classic form of maple syrup urine disease;Wang;Gene,2012

3. NM NL Identification of a novel homozygous mutation in a Malay patient with maple syrup urine disease;Ali;J Pediatr Endocrinol Metab,2013

4. case of reversible blindness in maple syrup urine disease;Backhouse,1999

5. Backe PH Four novel mutations identified in Norwegian patients result in intermittent maple syrup urine disease when combined with the mutation;Brodtkorb;Mol Genet Metab,2010

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