Reduced Protein Import via TIM23 SORT Drives Disease Pathology in TIMM50-Associated Mitochondrial Disease

Author:

Crameri Jordan J.12,Palmer Catherine S.12,Stait Tegan34,Jackson Thomas D.12,Lynch Matthew567,Sinclair Adriane5,Frajman Leah E.3,Compton Alison G.348,Coman David67,Thorburn David R.348,Frazier Ann E.38,Stojanovski Diana12

Affiliation:

1. Department of Biochemistry and Pharmacology, The University of Melbourne, Parkville, Victoria, Australia

2. The Bio21 Molecular Science and Biotechnology Institute, The University of Melbourne, Parkville, Victoria, Australia

3. Murdoch Children’s Research Institute, Royal Children’s Hospital, Parkville, Victoria, Australia

4. Victorian Clinical Genetics Services, Royal Children’s Hospital, Parkville, Victoria, Australia

5. Neurosciences Department, Queensland Children’s Hospital, South Brisbane, Queensland, Australia

6. Department of Metabolic Medicine, Queensland Children’s Hospital, South Brisbane, Queensland, Australia

7. School of Medicine, University of Queensland, St Lucia, Queensland, Australia

8. Department of Paediatrics, The University of Melbourne, Parkville, Victoria, Australia

Publisher

Informa UK Limited

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