Severe endothelial dysfunction in the aorta of a mouse model of Fabry disease; partial prevention by N-butyldeoxynojirimycin treatment
Author:
Publisher
Wiley
Subject
Genetics (clinical),Genetics
Link
http://www.springerlink.com/index/pdf/10.1007/s10545-006-0473-y
Reference35 articles.
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3. Barngrover D (2002) Fabrazyme—recombinant protein treatment for Fabry's disease. J Biotechnol 95: 280–282.
4. Bodary PF, Shen Y, Vargas FB, et al (2005) Alpha-galactosidase A deficiency accelerates atherosclerosis in mice with apolipoprotein E deficiency. Circulation 111: 629–632.
5. Boutouyrie P, Laurent S, Laloux B, et al (2001) Non-invasive evaluation of arterial involvement in patients affected with Fabry disease. J Med Genet 38: 629–631.
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