The consequences of genetic and pharmacologic reduction in sphingolipid synthesis
Author:
Publisher
Wiley
Subject
Genetics(clinical),Genetics
Link
http://link.springer.com/content/pdf/10.1007/s10545-014-9758-8
Reference90 articles.
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2. Aerts JM, Ottenhoff R, Powlson AS et al (2007) Pharmacological inhibition of glucosylceramide synthase enhances insulin sensitivity. Diabetes 56(5):1341–1349
3. Andersson U, Smith D, Jeyakumar M et al (2004) Improved outcome of N-butyldeoxygalactonojirimycin-mediated substrate reduction therapy in a mouse model of Sandhoff disease. Neurobiol Dis 16(3):506–515
4. Arthur JR, Wilson MW, Larsen SD, Rockwell HE, Shayman JA, Seyfried TN (2013) Ethylenedioxy-PIP2 oxalate reduces ganglioside storage in juvenile sandhoff disease mice. Neurochem Res 38(4):866–875
5. Ashe KM, Bangari D, Li L et al (2011) Iminosugar-based inhibitors of glucosylceramide synthase increase brain glycosphingolipids and survival in a mouse model of sandhoff disease. PLoS One 6(6):e21758
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