Bezafibrate lowers very long-chain fatty acids in X-linked adrenoleukodystrophy fibroblasts by inhibiting fatty acid elongation-Reference-Cited by-同舟云学术

Bezafibrate lowers very long-chain fatty acids in X-linked adrenoleukodystrophy fibroblasts by inhibiting fatty acid elongation

Published:2012-03-24 Issue:6 Volume:35 Page:1137-1145
ISSN:0141-8955
Container-title:Journal of Inherited Metabolic Disease
language:en
Short-container-title:J Inherit Metab Dis

Author:

Engelen Marc,Schackmann Martin J. A.,Ofman Rob,Sanders Robert-Jan,Dijkstra Inge M. E.,Houten Sander M.,Fourcade Stéphane,Pujol Aurora,Poll-The Bwee Tien,Wanders Ronald J. A.,Kemp Stephan

Publisher

Wiley

Subject

Genetics(clinical),Genetics

Link

http://www.springerlink.com/index/pdf/10.1007/s10545-012-9471-4

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5. Bonnefont JP, Bastin J, Behin A, Djouadi F (2009) Bezafibrate for an inborn mitochondrial beta-oxidation defect. N Engl J Med 360:838–840

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