Higher Vulnerability of Menadione-Exposed Cortical Astrocytes of Glutaryl-CoA Dehydrogenase Deficient Mice to Oxidative Stress, Mitochondrial Dysfunction, and Cell Death: Implications for the Neurodegeneration in Glutaric Aciduria Type I-Reference-Cited by-同舟云学术

Higher Vulnerability of Menadione-Exposed Cortical Astrocytes of Glutaryl-CoA Dehydrogenase Deficient Mice to Oxidative Stress, Mitochondrial Dysfunction, and Cell Death: Implications for the Neurodegeneration in Glutaric Aciduria Type I

Published:2016-08-10 Issue:6 Volume:54 Page:4795-4805
ISSN:0893-7648
Container-title:Molecular Neurobiology
language:en
Short-container-title:Mol Neurobiol

Author:

Rodrigues Marília Danyelle Nunes,Seminotti Bianca,Zanatta Ângela,de Mello Gonçalves Aline,Bellaver Bruna,Amaral Alexandre Umpierrez,Quincozes-Santos André,Goodman Stephen Irwin,Woontner Michael,Souza Diogo Onofre,Wajner Moacir

Funder

Conselho Nacional de Desenvolvimento Científico e Tecnológico

Fundação de Amparo à Pesquisa do Estado do Rio Grande do Sul

Universidade Federal do Rio Grande do Sul

Rede Instituto Brasileiro de Neurociência (IBNet/FINEP)

Instituto Nacional de Ciência e Tecnologia em Excitotoxicidade e Neorologia (INCT)

Publisher

Springer Science and Business Media LLC

Subject

Neuroscience (miscellaneous),Cellular and Molecular Neuroscience,Neurology

Link

http://link.springer.com/article/10.1007/s12035-016-0023-z/fulltext.html

Reference76 articles.

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3. Funk CB, Prasad AN, Frosk P, Sauer S, Kolker S, Greenberg CR, Del Bigio MR (2005) Neuropathological, biochemical and molecular findings in a glutaric acidemia type 1 cohort. Brain 128(Pt 4):711–722

4. Hoffmann GF, Zschocke J (1999) Glutaric aciduria type I: from clinical, biochemical and molecular diversity to successful therapy. J Inherit Metab Dis 22(4):381–391

5. Busquets C, Coll MJ, Merinero B, Ugarte M, Ruiz MA, Martinez Bermejo A, Ribes A (2000) Prenatal molecular diagnosis of glutaric aciduria type I by direct mutation analysis. Prenat Diagn 20(9):761–764

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