Hereditary hemorrhagic telangiectasia with hepatic arteriovenous shunt diagnosed due to liver damage

Author:

Hagiwara SatoruORCID,Takase Toru,Oda Itsuki,Komeda Yoriaki,Nishida Naoshi,Yoshida Akihiro,Yamamoto Tomoki,Matsubara Takuya,Kudo Masatoshi

Abstract

AbstractA 53-year-old woman was diagnosed with liver dysfunction in August 20XX. Computed tomography (CT) revealed multiple hepatic AV shunts, and she was placed under observation. In March 20XX + 3, she developed back pain, and CT performed during an emergency hospital visit showed evidence of intrahepatic bile duct dilatation. She was referred to our gastroenterology department in May 20XX + 3. We conducted investigations on suspicion of hereditary hemorrhagic telangiectasia (HHT) with hepatic AV shunting based on contrast-enhanced CT performed at another hospital. HHT is generally discovered due to epistaxis, but there are also cases where it is diagnosed during examination of liver damage.

Publisher

Springer Science and Business Media LLC

Reference19 articles.

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