Combined ankyrin and spectrin deficiency in hereditary spherocytosis
Author:
Publisher
Springer Science and Business Media LLC
Subject
Hematology,General Medicine
Link
http://link.springer.com/content/pdf/10.1007/BF01788132.pdf
Reference28 articles.
1. Agre P, Orringer EP, Bennett V (1982) Deficient red cell spectrin in severe recessively inherited hereditary spherocytosis. N Engl J Med 306:1155–1160
2. Agre P, Casella JF, Zinkham WH, McMillan C, Bennett V (1985) Partial deficiency of erythrocyte spectrin in hereditary spherocytosis. Nature 314:380–383
3. Agre P, Asiomo A, Casella JF, McMillan C (1986) Inheritance pattern and clinical response to splenectomy as a refluction of erythrocyte spectrin deficiency in hereditary spherocytosis. N Engl J Med 315:1579–1583
4. Becker PS, Morrow JS, Lux SE (1987) Abnormal oxidant sensitivity and β-chain structure of spectrin in hereditary spherocytosis associated with defective spectrin-protein 4.1 binding. J Clin Invest 80:557–565
5. Bennett V, Stenbuck PJ (1980) Association between ankyrin and the cytoplasmic domain of band 3 isolated from the human erythrocyte membrane. J Biol Chem 255:6424–6432
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