Neuroinflammation bei neuronalen Ceroid-Lipofuszinosen
Author:
Publisher
Springer Science and Business Media LLC
Subject
Ophthalmology
Link
http://link.springer.com/content/pdf/10.1007/s00347-020-01301-4.pdf
Reference46 articles.
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2. Atiskova Y, Bartsch S, Danyukova T et al (2019) Mice deficient in the lysosomal enzyme palmitoyl-protein thioesterase 1 (PPT1) display a complex retinal phenotype. Sci Rep 9(1):14185. https://doi.org/10.1038/s41598-019-50726-8
3. Augustine EF, Beck CA, Adams HR et al (2019) Short-term administration of mycophenolate is well-tolerated in CLN3 disease (juvenile neuronal ceroid lipofuscinosis). JIMD Rep 43:117–124
4. Benitez BA, Cairns NJ, Schmidt RE et al (2015) Clinically early-stage CSPα mutation carrier exhibits remarkable terminal stage neuronal pathology with minimal evidence of synaptic loss. acta neuropathol commun 3:73–73
5. Brooks AI, Chattopadhyay S, Mitchison HM et al (2003) Functional categorization of gene expression changes in the cerebellum of a Cln3-knockout mouse model for Batten disease. Mol Genet Metab 78:17–30
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