Fatal Congenital Systemic Juvenile Xanthogranuloma with Liver Failure-Reference-Cited by-同舟云学术

Fatal Congenital Systemic Juvenile Xanthogranuloma with Liver Failure

Published:2004-01 Issue:1 Volume:7 Page:71-76
ISSN:1093-5266
Container-title:Pediatric and Developmental Pathology
language:en
Short-container-title:Pediatr Dev Pathol

Author:

Hu Weimin K.¹,Gilliam Anita C.¹,Wiersma Susan R.²,Dahms Beverly B.³

Affiliation:

1. Department of Dermatology, University Hospitals of Cleveland and Case Western University School of Medicine, 11100 Euclid Avenue, Cleveland, OH 44106, USA

2. Department of Pediatrics, University Hospitals of Cleveland, 11100 Euclid Avenue, Cleveland, OH 44106, USA

3. Department of Pathology, University Hospitals of Cleveland, 11100 Euclid Avenue, Cleveland, OH 44106, USA

Abstract

This is the second reported patient with systemic juvenile xanthogranuloma (JXG) to die with liver failure. The infant was born with multiple skin lesions and mild hepatomegaly. Direct hyperbilirubinemia was noted on the 2nd day of life, followed by progressive hepatomegaly, cholestasis, and death at 29 days of age. At autopsy, nodular tumor infiltrates of JXG were present throughout the liver, as well as in skin, abdominal lymph nodes, spleen, and pancreas.

Publisher

SAGE Publications

Subject

General Medicine,Pathology and Forensic Medicine,Pediatrics, Perinatology, and Child Health

Link

http://journals.sagepub.com/doi/pdf/10.1007/s10024-003-4040-3

Reference21 articles.

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2. Juvenile xanthogranuloma: Forms of systemic disease and their clinical implications

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4. Juvenile Xanthogranulomas in the First Two Decades of Life: A Clinicopathologic Study of 174 Cases With Cutaneous and Extracutaneous Manifestations

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