Tauroursodeoxycholic bile acid arrests axonal degeneration by inhibiting the unfolded protein response in X-linked adrenoleukodystrophy-Reference-Cited by-同舟云学术

Tauroursodeoxycholic bile acid arrests axonal degeneration by inhibiting the unfolded protein response in X-linked adrenoleukodystrophy

Published:2016-12-21 Issue:2 Volume:133 Page:283-301
ISSN:0001-6322
Container-title:Acta Neuropathologica
language:en
Short-container-title:Acta Neuropathol

Author:

Launay Nathalie,Ruiz Montserrat,Grau Laia,Ortega Francisco J.,Ilieva Ekaterina V.,Martínez Juan José,Galea Elena,Ferrer Isidre,Knecht Erwin,Pujol Aurora^ORCID,Fourcade Stéphane

Funder

European Commission

European Leukodystrophy Association

Spanish Institute for Health Carlos III and ‘Fondo Europeo de Desarrollo Regional

Autonomous Government of Catalonia

The Spanish Institute for Health Carlos III

Center for Biomedical Research on Rare Diseases

Spanish Institute for Health Carlos III and Fondo Europeo de Desarrollo Regional

Publisher

Springer Science and Business Media LLC

Subject

Cellular and Molecular Neuroscience,Neurology (clinical),Pathology and Forensic Medicine

Link

http://link.springer.com/content/pdf/10.1007/s00401-016-1655-9.pdf

Reference106 articles.

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4. Bellentani S, Chao YC, Ferretti I, Panini R, Tiribelli C (1996) Chronic administration of ursodeoxycholic and tauroursodeoxycholic acid changes microsomal membrane lipid content and fatty acid compositions in rats. Biochem Biophys Res Commun 220:479–483

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