Postoperative metabolic decompensation in maple syrup urine disease is completely prevented by insulin-Reference-Cited by-同舟云学术

Postoperative metabolic decompensation in maple syrup urine disease is completely prevented by insulin

Published:1993 Issue:5 Volume:16 Page:912-913
ISSN:0141-8955
Container-title:Journal of Inherited Metabolic Disease
language:en
Short-container-title:J Inherit Metab Dis

Author:

Biggemann B.,Zass R.,Wendel U.

Publisher

Wiley

Subject

Genetics (clinical),Genetics

Link

http://www.springerlink.com/index/pdf/10.1007/BF00714298

Reference4 articles.

1. Berry GT, Heidenreich R, Kaplan P et al (1991) Branched-chain amino acid-free parenteral nutrition in the treatment of acute metabolic decompensation in patients with maple syrup urine disease.N Engl J Med 324: 175?179.

2. Castellino P, Luzi L, Simonson DC, Haymond M, De Fronzo RA (1987) Effect of insulin and plasma amino acid concentrations on leucine metabolism in man.J Clin Invest 80: 1784?1793.

3. Fiedler AE, Miller MJ, Bickel H, Cederbaum SD (1982) Phenylalanine levels in PKU following minor surgery.Am J Med Genet 11: 411?414.

4. Tessari P, Trevisan R, Inchiostro S et al (1986) Dose-response curves of effects of insulin on leucine kinetics in humans.Am J Physiol 251: E334?342.

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