STURGE WEBER SYNDROME: A CASE REPORT WITH CLINICAL AND RADIOLOGICAL FEATURES

Abstract

Sturge–Weber syndrome, also referred to as encephalotrigeminal angiomatosis, is a rare congenital neurological and skin disorder. It is one of the phakomatoses and is often associated with port-wine stains of the face, glaucoma, seizures, mental retardation, and ipsilateral leptomeningeal angioma (cerebral malformations and tumors). It is characterized by abnormal blood vessels on the brain surface. We report a case of 8 year old male child with facial port wine stains along with radiological features which showed tram track sign and cortical atrophy in the right temporo-parieto- occipital lobe.