CHRONIC MYELOID LEUKEMIA IN A PATIENT WITH ABDOMINAL COCOON SYNDROME: A RARE CLINICAL PRESENTATION

Abstract

Described for the rst time almost a century ago, Sclerosing Encapsulating Peritonitis (SEP) is characterized by development of membrane like structure around abdominal viscera, especially small bowel. It is a recognized, rare cause of intestinal obstruction. Though several malignancies have been described as risk factors for SEP, contribution of these are on the lower side and most of these are abdominal malignancies if not all. Association of leukemias or lymphomas with SEP could not be found in literature. Our patient is an 18-year-old boy, who presented with complaints of abdominal pain and vomiting. He was managed conservatively, and relevant blood investigations and imaging was done. Ultrasound of abdomen and subsequent Contrast Enhanced CT scan of abdomen conrmed SEP, whereas blood investigations conrmed diagnosis of Chronic Myeloid Leukemia. Chronic myeloid leukemia predominantly occurs in elderly males with mean age of 65 or more. CML in young patient is a rare occurrence, that coupled with occurrence of SEP makes this case unique.