Affiliation:
1. Professor & HOD, Department of Radiology, Mandya Institute of Medical Sciences, Mandya, Karnataka, India
2. Associate Professor, Department of Radiology, Mandya Institute of Medical Sciences, Mandya, Karnataka, India
3. Assistant Professor, Department of Forensic Medicine, Adichunchanagiri Institute of Medical Sciences, BG Nagar, Mandya District, Karnataka, India
Abstract
Achalasia is an esophageal motility disorder with progressive
dysphagia for liquids and solids. It occurs due to absence or
degeneration of myenteric plexus of nerves in the distal
esophagus. The term pseudoachalasia refers to achalasia like
symptoms and imaging manifestations caused by diseases
other than aganglionosis [1]. It can be due to stricture,
extrinsic compression, malignant neoplasm or proliferation
of smooth muscle cells as in leiomyomatosis. Diffuse
leiomyomatosis of the esophagus is a very rare cause of
pseudoachalasia and requires total esophagectomy with
gastric pull through surgery. We present a rare case of a seven
year old boy with diffuse leiomyomatosis of esophagus
presenting with pseudoachalasia, aspiration pneumonitis and
bronchiectasis secondary to recurrent aspirations.
Subject
Immunology,General Medicine,Immunology and Allergy,Cancer Research,Public Health, Environmental and Occupational Health,Oncology,Epidemiology,Biochemistry, Genetics and Molecular Biology (miscellaneous),Infectious Diseases,Microbiology (medical),General Medicine,Philosophy,Religious studies,Political Science and International Relations,Sociology and Political Science,Demography,Finance,Accounting,Sociology and Political Science,History,Cultural Studies
Reference15 articles.
1. Kahrilas PJ, Kishk SM, Helm JF, Dodds WJ, Harig JM, Hogan WJ. Comparison of pseudoachalasia and achalasia. Am J Med. 1987 Mar;82(3):439-46.
2. Sica GS, Sujendran V, Warren B, Maynard ND. Neurofibromatosis of the esophagus. Ann Thorac Surg. 2006 Mar; 81(3):1138-40.
3. Pesce A, Scilletta R, Branca A, Portale TR, Puleo S. A rare case of pancreatic cancer presenting as pseudoachalasia. Ann Ital Chir. 2012 Sep 10;2012.
4. Saino G, Bona D, Nencioni M, Rubino B, Bonavina L. Laparoscopic diagnosis of pleural mesothelioma presenting with pseudoachalasia. World J Gastroenterol. 2009 Jul 28; 15(28):3569-72.
5. Hall A. A case of diffuse fibromyoma of the esophagus, causing dysphagia and death. Q J Med 1916;9:409-28.