MATERNAL TUBEROUS SCLEROSIS WITH FETAL CARDIAC RHABDOMYOMA – A CASE REPORT-Reference-Cited by-同舟云学术

MATERNAL TUBEROUS SCLEROSIS WITH FETAL CARDIAC RHABDOMYOMA – A CASE REPORT

Published:2021-06-15 Issue: Volume: Page:28-30
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Container-title:GLOBAL JOURNAL FOR RESEARCH ANALYSIS
language:en
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Author:

Rama Harikanth Disha¹,Waikar Manjushri²

Affiliation:

1. MBBS, Junior Resident (MS OBGY) Department of Obstretrics and Gynaecology,Government Medical College Nagpur,India

2. MBBS, MS, Professor, Department of Obstretrics and Gynaecology, Government Medical College Nagpur, India.

Abstract

Tuberous sclerosis is a multisystemic, autosomal dominant neurocutaneous disorder of hamartoma formation affecting multiple organ systems and hence adversely affecting the maternal and fetal outcome. We report a case of maternal tuberous sclerosis with fetal cardiac rhabdomyoma detected in utero at 22 weeks but presented at 39 weeks of gestation. We conclude that Maternal or Fetal tuberous sclerosis deserves careful monitoring and evaluation so that the patients can be counselled regarding its life threatening complications to the baby and make informed decision regarding continuation of pregnancy

Publisher

World Wide Journals

Reference10 articles.

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