LEFT VENTRICULAR NON-COMPACTION CARDIOMYOPATHY IN THE REAL LIFE-Reference-Cited by-同舟云学术

LEFT VENTRICULAR NON-COMPACTION CARDIOMYOPATHY IN THE REAL LIFE

Published:2021-03-01 Issue: Volume: Page:33-35
ISSN:
Container-title:INDIAN JOURNAL OF APPLIED RESEARCH
language:en
Short-container-title:IJAR

Author:

Bensahi I.¹,Elharras M.²,Merzouk Fz.¹,Elouarradi A.³,Sabry M.³

Affiliation:

1. Pôle de Cardiologie clinique et interventionnelle, Faculté de Médecine-Université Med VI des Sciences de la Santé- Hôpital Universitaire International Cheikh KhalifaCasablanca/MAROC.

2. Pôle de Cardiologie clinique et interventionnelle,Faculté de Médecine-Université Med VI des Sciences de la Santé- Hôpital Universitaire International Cheikh KhalifaCasablanca/MAROC.

3. Pôle de Cardiologie clinique et interventionnelle, Faculté de Médecine-Université Med VI des Sciences de la Santé- Hôpital Universitaire International Cheikh KhalifaCasablanca/MAROC

Abstract

Left ventricular non-compaction (LVNC) is a very rare congenital cardiomyopathy which is treated recently as an unclassied cardiomyopathy by the European Society of Cardiology while the American Heart Association includes it among genetic cardiomyopathies. It is characterized by prominent endomyocardial trabeculations that increase in number and deep intertrabecular recesses. In this article we will report the case of a 55 years old man patient diagnosed since 2014 with an isolated LVNC with ascites and edema of the lower limbs despite high doses of loop diuretcs illustrating the limited therapeutic options of this kind of cardiomyopathy

Publisher

World Wide Journals

Reference12 articles.

1. Maron, B.J. Towbin, J.A. Thiene, G. Antzelevitch, C. Corrado, D. Contemporary definitions and classification of the cardiomyopathies : An American Heart Association Scientific Statement from the Council on Clinical Cardiology, Heart Failure and Transplantation Committee; Quality of Care and Outcomes Research and Functional Genomics and Translational Biology Interdisciplinary Working Groups; and Council on Epidemiology and Prevention. Circulation 2006, 113, 1807–1816. [PubMed]

2. Abustini, E. Weidemann, F. Hall, J.L. Left ventricular non-compaction : A distinct cardiomyopathy or a trait sharded by different cardiac disease. J. Am. Coll. Cardiol. 2014, 64, 1840–1850

3. Richard P, Ader F, Roux M, Donal E, Eicher JC, Aoutil N, Huttin O, Selton-Suty C, Coisne D, Jondeau G, Damy T, Mansencal N, Casalta AC, Michel N, Haentjens J, Faivre L, Lavoute C, Nguyen K, Tregouët DA, Habib G, Charron P. Targeted panel sequencing in adult patients with left ventricular non-compaction reveals a large genetic heterogeneity. Clin Genet. 2019 Mar;95(3):356-367.

4. Hirono K, Hata Y, Nakazawa M, Momoi N, Tsuji T, Matsuoka T, Ayusawa M, Abe Y, Hayashi T, Tsujii N, Abe T, Sakaguchi H, Wang C, Takasaki A, Takarada S, Okabe M, Miyao N, Nakaoka H, Ibuki K, Saito K, Ozawa S, Nishida N, Bowles NE, Ichida F. Clinical and Echocardiographic Impact of Tafazzin Variants on Dilated Cardiomyopathy Phenotype in Left Ventricular Non-Compaction Patients in Early Infancy. Circ J. 2018 Sep 25;82(10):2609-2618.

5. Parekh JD, Iguidbashian J, Kukrety S, Guerins K, Millner PG, Andukuri V. A Rare Case of Isolated Left Ventricular Non-compaction in an Elderly Patient. Cureus. 2018 Jun 26;10(6):e2886.