“RARE TUMOUR OF THE HAND: MALIGNANT ACROSPIROMA OF THE HAND“

Abstract

Background: Malignant acrospiroma is among one of the rare tumors of the eccrine sweat glands. It accounts for around 6% of all malignant eccrine tumors. It typically presents as large ulcerated nodules, and diagnosis can be challenging as it has great overlap with its benign counterpart. There are limited cases reported for hand acrospiroma’s. Case presentation: We report a case of malignant acrospiroma presenting as swelling which was treated with surgical excision. The patient was referred to oncosurgery for chemoradiaton. Conclusion: Wide surgical excision, with or without prophylactic lymph node dissection, is the treatment of choice. Evidence is lacking on the efficacy and/or advised regimen of chemoradiotherapy. Prognosis is poor with systemic disease. More studies are needed for the management of this disease.