A RARE CASE OF UNDIFFERENTIATED EMBRYONAL SARCOMA OF LIVER IN 8 YEAR FEMALE CHILD

Abstract

Introduction: Undifferentiated embryonal sarcoma of liver (USEL) is a rare disease that 90% occurs in children between age group 6-10 years with no gender discrepancy. Diagnosis of USEL relies on postoperative pathology and immunohistochemistry. Objective : This is a rare case report of an 8 year female patient who underwent excision of liver mass with left side lobectomy for a liver mass which turned out to be Undifferentiated Embryonal Sarcoma of Liver(USEL) on Histopathological analysis and Immunohistochemical examination. Results : Patient was diagnosed to be having Gastrointestinal Stromal Tumor of stomach on radiological investigations but intraoperatively turned out to be a liver mass for which patient underwent excision of liver mass with left side lobectomy for a liver mass which turned out to be Undifferentiated Embryonal Sarcoma of Liver(USEL) on Histopathological analysis and Immunohistochemical examination. Patient underwent chemotherapy including ifosfamide, mesna and doxorubicin. Currently, the patient’s physical status is normal with no distant metastases shown in PET-CT. Conclusion : Undifferentiated Embryonal Sarcoma of Liver is a rare entity but with adequate surgical procedure and followup chemotherapy or radiotherapy has excellent prognosis