Ectodermal Dysplasia Presenting with Atrophic Rhinitis: Report of Two Cases and Review of Literature

Abstract

ABSTRACT Aim To present two rare case of ectodermal dysplasia presenting with maggot infestation due to atrophic rhinitis. Study design Case report. Setting Tertiary care referral hospital. Presentation Two male child aged about 5 and 8 years presented in ENT emergency with history of maggot infestation of nose. Result Clinical examination was suggestive of ectodermal dysplasia. Intranasal examination was suggestive of atrophic rhinitis. Maggots were removed in conventional manner. Following conservative treatment, skin biopsy and nasal mucosal biopsy was taken which confirmed the diagnosis of ectodermal dysplasia. Conclusion Any ectodermal dysplasia patient should be suspected of having atrophic rhinitis and intranasal conservative therapy should be initiated at the earliest to prevent complication like maggots in nose. How to cite this article Pati S, Pal S, Saha S, Biswas S. Ectodermal Dysplasia Presenting with Atrophic Rhinitis: Report of Two Cases and Review of Literature. Clin Rhinol An Int J 2015;8(3):133-135.