A Simplified Basic Classification of Spatial Alignments of the Heart, Its Chambers, and the Great Vessels

Abstract

The problems resulting from a lack of accepted terminology and a basic classification system for the various spatial alignments of the heart, its chambers and great vessels are reviewed. A basic simplified classification system founded on fundamental embryologic, clinical, and roentgenologic considerations is proposed. Terminology employed is precisely defined. The clinical studies needed to place patients in their category are enumerated and discussed. It is recognized that some forms of spatial derangement defy classification within this system. Nevertheless, this classification system with the suggested terminology, however inadequate, is offered as a means to promote clinical definition of these entities and to encourage clear discussion and a better understanding of these conditions. It is hoped that future study will add to our knowledge of the embryologic mechanisms involved and eventually lead to a more comprehensive classification embracing a larger number of congenital cardiac anomalies.