Author:
Deng Minying,Liu Qingxiao,Ren Lei,Yuan Wei,Xu Chen,Hou Yingyong
Abstract
AbstractDermatofibrosarcoma protuberans (DFSP) is a low-grade malignant soft-tissue tumor that originates from the skin. It has a slow onset in the early stages, non-specific clinical symptoms, low specificity, and can easily be overlooked, missed, or misdiagnosed by clinicians and pathologists. In addition, DFSP is prone to recurrence after local surgical treatment; however, distant metastasis, especially abdominal metastasis, is rare, which is also a challenge for the accurate diagnosis of DFSP when it progresses distantly. Now a case of abdominal metastasis of DFSP is reported. The patient has been treated with imatinib for ten years, and the lesion has shrunk, but because the patient has been receiving imatinib treatment, his abdominal lesion was once misdiagnosed as gastrointestinal stromal tumor. Therefore, we report on this case to enhance the understanding of the diagnosis and treatment of DFSP, and to provide reference for the pathological diagnosis and precise treatment of such patients.
Funder
2023 National Key Clinical Specialty - Pathology Next Generation Oncological Disease Integrated Pathological Diagnosis
Shanghai Clinical Specialty Construction Project
Shanghai Science and Technology Innovation Action Plan Natural Science Fund Project in 2023
Publisher
Springer Science and Business Media LLC
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