1. Institute of Inherited Metabolic Disorders, First Medical Faculty, Charles University in Prague and General University Hospital in Prague, Ke Karlovu 2, Prague 2, 128 00 Czech Republic
2. Department of Biochemistry and Microbiology, Institute of Chemical Technology in Prague, Technická 5, Prague 6, 166 28 Czech Republic
3. Department of Pediatrics, University of Colorado School of Medicine, Aurora, Colorado 80045, United States