Author:
Basu Suprit,Tyagi Reva,Jindal Ankur Kumar,Medha Apurva,Banday Aaqib Zaffar,Babbar Alisha,Sharma Apoorva,Mahajan Rahul,Vignesh Pandiarajan,Rawat Amit
Abstract
Papillon–Lefèvre syndrome (PLS) is a rare autosomal recessive disorder characterized clinically by palmoplantar keratoderma, periodontitis, and recurrent pyogenic infections. Liver abscess is rarely reported in patients. The use of corticosteroids for the treatment of liver abscess akin to chronic granulomatous disease (CGD) has not been reported previously. Here, we report 2 cases of liver abscess in PLS that responded to corticosteroids.
Subject
Pediatrics, Perinatology and Child Health