Treatment and management of primary antibody deficiency: German interdisciplinary evidence‐based consensus guideline

Author:

Hanitsch Leif1ORCID,Baumann Ulrich2,Boztug Kaan3,Burkhard‐Meier Ulrike4,Fasshauer Maria5,Habermehl Pirmin6,Hauck Fabian7,Klock Gerd8,Liese Johannes9,Meyer Oliver10,Müller Rainer11,Pachlopnik‐Schmid Jana12,Pfeiffer‐Kascha Dorothea13,Warnatz Klaus1415,Wehr Claudia1516,Wittke Kirsten1,Niehues Tim17ORCID,Bernuth Horst181920

Affiliation:

1. Institute for Medical Immunology Charité Universitaetsmedizin Berlin Berlin Germany

2. Department of Paediatric Pulmonology Allergy and Neonatology Hannover Medical School Hannover Germany

3. CeMM Research Center for Molecular Medicine of the Austrian Academy of Sciences Ludwig Boltzmann Institute for Rare and Undiagnosed Diseases Department of Pediatrics and Adolescent Medicine and St. Anna Kinderspital and Children's Cancer Research Institute Department of Pediatrics Medical University of Vienna Vienna Austria

4. Praxis für Hämatologie und Onkologie Mönchengladbach Germany

5. ImmunoDeficiencyCenter Leipzig (IDCL) Hospital St. Georg gGmbH Leipzig Academic Teaching Hospital of the University of Leipzig Leipzig Germany

6. Kinderarztpraxis Mainz‐Hechtsheim Germany

7. Department of Pediatrics Dr. von Hauner Children's Hospital University Hospital Ludwig‐Maximilians‐University Munich Munich Germany

8. Technische Universität Darmstadt Clemens‐Schöpf‐Institut für Organische Chemie & Biochemie Darmstadt Germany

9. Pediatric Immunology Department of Pediatrics University Hospital Würzburg Würzburg Germany

10. Institute of Transfusion Medicine Charité ‐ Universitätsmedizin Berlin Berlin Germany

11. Klinik und Poliklinik für HNO‐Heilkunde Universitätsklinikum Carl Gustav Carus an der Technischen Universität Dresden Dresden Germany

12. Division of Immunology University Children‘s Hospital Zurich and University of Zurich Switzerland

13. AG Atemphysiotherapie Physiotherapiepraxis Röske Wuppertal Germany

14. Department of Rheumatology and Clinical Immunology Medical Center ‐ University of Freiburg Faculty of Medicine University of Freiburg Freiburg Germany

15. Center for Chronic Immunodeficiency Medical Center ‐ University of Freiburg Faculty of Medicine University of Freiburg Freiburg Germany

16. Department of Medicine I Medical Center – University of Freiburg Faculty of Medicine University of Freiburg Freiburg Germany

17. Department of Pediatrics Helios Klinikum Krefeld Krefeld Germany

18. Department of Immunology Labor Berlin Charité ‐ Vivantes GmbH Berlin Germany

19. Berlin Center for Regenerative Therapies (BCRT) Charité Universitätsmedizin Berlin Berlin Germany

20. Department of Pediatric Pneumology Immunology and Intensive Care Medicine Charité Universitätsmedizin Berlin Berlin Germany

Publisher

Wiley

Subject

Immunology,Immunology and Allergy

Reference141 articles.

1. Human inborn errors of immunity: 2019 update of the IUIS phenotypical classification;Bousfiha A.;J. Clin. Immunol.,2020

2. Clinical picture and treatment of 2212 patients with common variable immunodeficiency;Gathmann B.;J. Allergy Clin. Immunol.,2014

3. Infections in 252 patients with common variable immunodeficiency;Oksenhendler E.;Clinical infectious diseases: an official publication of the Infectious Diseases Society of America,2008

4. Treatment and outcome of autoimmune hematologic disease in common variable immunodeficiency (CVID);Wang J.;J. Autoimmun.,2005

5. Interstitial Lung Disease Frequently Precedes CVID Diagnosis;Hanitsch L. G.;J. Clin. Immunol.,2019

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