An autopsy report of three kindred in a Gerstmann-Sträussler-Scheinker disease P105L family with a special reference to prion protein, tau, and beta-amyloid-Reference-Cited by-同舟云学术

An autopsy report of three kindred in a Gerstmann-Sträussler-Scheinker disease P105L family with a special reference to prion protein, tau, and beta-amyloid

Published:2018-09-21 Issue:10 Volume:8 Page:e01117
ISSN:2162-3279
Container-title:Brain and Behavior
language:en
Short-container-title:Brain Behav

Author:

Ishizawa Keisuke¹²^ORCID,Mitsufuji Takashi¹,Shioda Kei²,Kobayashi Atsushi³,Komori Takashi⁴,Nakazato Yoshihiko¹,Kitamoto Tetsuyuki⁵,Araki Nobuo¹,Yamamoto Toshimasa¹,Sasaki Atsushi²

Affiliation:

1. Department of Neurology; Saitama Medical University; Saitama Japan

2. Department of Pathology; Saitama Medical University; Saitama Japan

3. Hokkaido University Graduate School of Veterinary Medicine; Hokkaido Japan

4. Department of Pathology; Tokyo Metropolitan Neurological Hospital; Tokyo Japan

5. Division of CJD Science and Technology, Department of Prion Research, Center for Translational and Advanced Animal Research on Human Diseases; Tohoku University Graduate School of Medicine; Miyagi Japan

Publisher

Wiley

Subject

Behavioral Neuroscience

Link

http://onlinelibrary.wiley.com/wol1/doi/10.1002/brb3.1117/fullpdf

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3. Beta PP participates in PrP-amyloid plaques of Gerstmann-Sträussler-Scheinker disease, Indiana kindred;Bugiani;Journal of Neuropathology & Experimental Neurology,1993

4. Gerstmann-Sträussler-Scheinker: A new phenotype with 'curly' PrP deposits;Colucci;Journal of Neuropathology & Experimental Neurology,2006

5. Pathological inclusion bodies in tauopathies contain distinct complements of tau with three or four microtubule-binding repeat domains as demonstrated by new specific monoclonal antibodies;Silva;Neuropathology and Applied Neurobiology,2003

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