Erdheim-Chester Disease and Small Lymphocytic Lymphoma Collision Tumour Presenting as a Perirenal Mass

Author:

Maietta Antonio1ORCID,Razmpoosh Maryam1

Affiliation:

1. Centre Hospitalier de l’université de Montréal (CHUM), 1100, rue Sanguinet, 7th Floor, F Pavillon, (Québec), Montréal, Canada H2X 0C1

Abstract

Background. Erdheim-Chester disease is a rare histiocytic neoplasm associated with MAPK pathway mutations. Disease manifestation is variable often involving many different organs, mainly bone, retroperitoneum, the heart, and the central nervous system. Histological findings include foamy histiocytes in a fibrous stroma with scattered inflammatory infiltrate. Histiocytes are CD68 positive and S100 negative. Case Report. We report a case of Erdheim-Chester disease associated with small lymphocytic lymphoma presenting as a perirenal mass with a review of the recent literature. Conclusions. Erdheim-Chester disease rarely can be associated with other cancers, namely myeloid neoplasms. We report a case of Erdheim-Chester disease presenting with small lymphocytic lymphoma as a perirenal mass. The association of Erdheim-Chester disease with lymphoproliferative disorders needs to be elucidated.

Publisher

Hindawi Limited

Subject

General Medicine

Cited by 2 articles. 订阅此论文施引文献 订阅此论文施引文献,注册后可以免费订阅5篇论文的施引文献,订阅后可以查看论文全部施引文献

1. Erdheim Chester Disease Mimicking Lymphoma: A Case Report;RöFo - Fortschritte auf dem Gebiet der Röntgenstrahlen und der bildgebenden Verfahren;2021-10-14

2. Erdheim-Chester Disease: a comprehensive review from the ophthalmologic perspective;Survey of Ophthalmology;2021-05

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