Herlyn-Werner-Wunderlich Syndrome Accompanying Hemosalpinx and Endometriotic Ovarian Cyst suspected as Tubo-Ovarian Abscess: A Rare Congenital Anomaly of Genitourinary System in a 12-year-old Female Patient

Abstract

Introduction: The Herlyn-Werner-Wunderlich (HWW) syndrome is a very rare congenital anomaly of the Mullerian duct and Wolffian duct with three symptoms of uterus: didelphys, obstructed hemivagina, and ipsilateral renal agenesis. In this syndrome, hydrometrocolpos or hematocolpometra, which are clinically equivalent to colpatresia, causes mass and pain. Case Presentation: This case reports a case of HWW syndrome with a left adnexal mass suspected as a tubo-ovarian abscess found on an abdominal CT image in a 12-year-old female patient who visited our hospital with the main complaint of lower abdominal pain and fever. Conclusion: A patient with HWW syndrome may be admitted to the emergency room with abdominal pain, though it is a rare case. This syndrome is manifested as abdominal pain and a mass due to hematocolpometra, mainly in women after puberty. For an adolescent female with ipsilateral renal agenesis accompanied by abdominal pain and mass, the diagnostic imaging test may be performed, considering HWW syndrome and precise surgical treatment should be planned.