A Variant of Gorlin–Goltz Syndrome with Synchronous Malignant and Multiple Benign Lesions of the Jaws

A Variant of Gorlin–Goltz Syndrome with Synchronous Malignant and Multiple Benign Lesions of the Jaws - A Case Report

Published:2023-10 Issue:4 Volume:34 Page:451-454
ISSN:0970-9290
Container-title:Indian Journal of Dental Research
language:en
Short-container-title:

Author:

John Reena R.¹,Ashokkumar Pavithran¹,Gopalakrishnan Kathirvel¹,Subramanian Mohithan²

Affiliation:

1. Department of Oral and Maxillofacial Surgery, Vinayaka Mission’s Sankarachariyar Dental College, Vinayaka Mission’s Research Foundation (Deemed to be University) Salem, Tamil Nadu, India

2. Department of Oral Medicine and Radiology, Vinayaka Mission’s Sankarachariyar Dental College, Vinayaka Mission’s Research Foundation (Deemed to be University) Salem, Tamil Nadu, India

Abstract

Introduction: Although numerous syndromic and non-syndromic odontogenic lesions of the jaws have been documented in the literature, there are very few cases of simultaneous benign and malignant jaw lesions. Patient Concerns: We present a case of right maxillary squamous cell carcinoma along with several benign odontogenic cystic lesions of the jaws and skeletal abnormalities that meet the criteria for Gorlin-Goltz syndrome. Take-Away Lessons: With a review of the literature, the specifics of management and follow-up are discussed.

Publisher

Medknow

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