CFTR-function and ventilation inhomogeneity in individuals with cystic fibrosis
Author:
Publisher
Elsevier BV
Subject
Pulmonary and Respiratory Medicine,Pediatrics, Perinatology and Child Health
Reference44 articles.
1. Defining the disease liability of variants in the cystic fibrosis transmembrane conductance regulator gene;Sosnay;Nat Genet,2013
2. Year to year change in FEV1in patients with cystic fibrosis and different mutation classes;De Boeck;J Cyst Fibros,2017
3. Practicability of nitrogen multiple-breath washout measurements in a pediatric cystic fibrosis outpatient setting;Singer;Pediatr Pulmonol,2013
4. Progressive ventilation inhomogeneity in infants with cystic fibrosis after pulmonary infection;Simpson;Eur Respir J,2015
5. Lung Clearance index and structural lung disease on computed tomography in early cystic fibrosis;Ramsey;Am J Respir Crit Care Med,2015
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1. Lung clearance index in children with cystic fibrosis previously diagnosed with CRMS/CFSPID: A monocentric prospective experience;Pediatric Pulmonology;2023-05-03
2. A New Era for Cystic Fibrosis and Cystic Fibrosis Transmembrane Conductance Regulator Modulator Trials in Infants;American Journal of Respiratory and Critical Care Medicine;2022-11-15
3. Association of lung clearance index with survival in individuals with cystic fibrosis;European Respiratory Journal;2021-07-21
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5. TOPIC SESSIONS;Pediatric Pulmonology;2021-06
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