Juvenile form of mucopolysaccharidosis VI (Maroteaux-Lamy syndrome). A C-terminal extension causes instability but increases catalytic efficiency of arylsulfatase B-Reference-Cited by-同舟云学术

Juvenile form of mucopolysaccharidosis VI (Maroteaux-Lamy syndrome). A C-terminal extension causes instability but increases catalytic efficiency of arylsulfatase B

Published:1994-04 Issue:13 Volume:269 Page:9638-9643
ISSN:0021-9258
Container-title:Journal of Biological Chemistry
language:en
Short-container-title:Journal of Biological Chemistry

Author:

Arlt G.,Brooks D.A.,Isbrandt D.,Hopwood J.J.,Bielicki J.,Bradford T.M.,Bindloss-Petherbridge C.A.,von Figura K.,Peters C.

Publisher

Elsevier BV

Subject

Cell Biology,Molecular Biology,Biochemistry

Reference31 articles.

1. A specific fluorogenic assay for N-acetylgalactosamine-4-sulphatase activity using immunoadsorption

2. Hurler syndrome: A patient with abnormally high levels of α-l-iduronidase protein

3. Effect of dystrophin gene deletions on mRNA levels and processing in Duchenne and Becker muscular dystrophies

4. Isolation of biologically active ribonucleic acid from sources enriched in ribonuclease

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