hiPSC hepatocyte model demonstrates the role of unfolded protein response and inflammatory networks in α1-antitrypsin deficiency-Reference-Cited by-同舟云学术

hiPSC hepatocyte model demonstrates the role of unfolded protein response and inflammatory networks in α1-antitrypsin deficiency

Published:2018-10 Issue:4 Volume:69 Page:851-860
ISSN:0168-8278
Container-title:Journal of Hepatology
language:en
Short-container-title:Journal of Hepatology

Author:

Segeritz Charis-Patricia,Rashid Sheikh Tamir,de Brito Miguel Cardoso,Serra Maria Paola,Ordonez Adriana,Morell Carola Maria,Kaserman Joseph E.,Madrigal Pedro,Hannan Nicholas R.F.,Gatto Laurent,Tan Lu,Wilson Andrew A.,Lilley Kathryn,Marciniak Stefan J.,Gooptu Bibek,Lomas David A.,Vallier Ludovic

Funder

Children’s Liver Disease Foundation

Medical Research Council

Wellcome Trust

GlaxoSmithKline

Rosetrees Trust

EPSRC

UCLH NIHR Biomedical Research Centre

ERC Relieve-IMDs

ERC

Cambridge University Hospitals National Institute for Health Research Biomedical Research Centre

MRC Clinician Scientist Fellowship

Publisher

Elsevier BV

Subject

Hepatology

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3. Alpha1-antitrypsin deficiency. 1: Epidemiology of alpha1-antitrypsin deficiency;Luisetti;Thorax,2004

4. Deficiency mutations of alpha-1 antitrypsin. Effects on folding, function, and polymerization;Haq;Am J Respir Cell Mol Biol,2016

5. Molecular pathogenesis of alpha-1-antitrypsin deficiency;Duvoix;Rev Mal Respir,2014

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