Glycosaminoglycan-Mediated Loss of Cathepsin K Collagenolytic Activity in MPS I Contributes to Osteoclast and Growth Plate Abnormalities
Author:
Publisher
Elsevier BV
Subject
Pathology and Forensic Medicine
Reference47 articles.
1. The Mucopolysaccharidoses;Neufeld,2001
2. Enzyme reconstitution/replacement therapy for lysosomal storage diseases;Burrow;Curr Opin Pediatr,2007
3. The role of cathepsins in osteoporosis and arthritis: rationale for the design of new therapeutics;Yasuda;Adv Drug Deliv Rev,2005
4. Pycnodysostosis, a lysosomal disease caused by cathepsin K deficiency;Gelb;Science,1996
5. Cathepsin K deficiency in pycnodysostosis results in accumulation of non-digested phagocytosed collagen in fibroblasts;Everts;Calcif Tissue Int,2003
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