Author:
Pellett Ocean L.,Smith Margaret L.,Thoene Smith Jess G.,Schneider Jerry A.,Jonas Adam J.
Publisher
Springer Science and Business Media LLC
Subject
Plant Science,Biotechnology,Plant Science,Biotechnology,Cell Biology,Clinical Biochemistry,Developmental Biology
Reference14 articles.
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2. Thoene, J. G.; Oshima, R. G.; Crawhall, J. C.; Olson, D. L.; Schneider, J. A. Cystinosis: Intracellular cystine depletion by aminothiols, in vitro and in vivo. J. Clin. Invest. 58: 180–189; 1976.
3. Yudkoff, M.; Foreman, J. W.; Segal, S. Effects of cysteamine therapy in nephropathic cystinosis. N. Engl. J. Med. 304: 141–145; 1981.
4. Thoene, J.; Gahl, W.; Rizzo, W.; Schulman, J. D.; Reed, G.; Denman, D.; Schlesselman, J.; Jonas, A.; Schneider, J. A. Cysteamine therapy of nephropathic cystinosis: Evidence for effectiveness. Pediatr. Res. 17: 220A; 1983.
5. Butler, J. DeB.; Zatz, M. Pantethine depletes cystinotic fibroblasts of cystine. J. Pediatr. 102: 796–798; 1983.
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