Are Astrocytes the Missing Link Between Lack of Brain Aspartoacylase Activity and the Spongiform Leukodystrophy in Canavan Disease?
Author:
Publisher
Springer Science and Business Media LLC
Subject
Cellular and Molecular Neuroscience,General Medicine,Biochemistry
Link
http://link.springer.com/content/pdf/10.1007/s11064-009-9958-z.pdf
Reference53 articles.
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2. Janson CG, McPhee SWJ, Francis J (2006) Natural history of Canavan disease revealed by proton magnetic resonance spectroscopy (1H-MRS) and diffusion-weighted MRI. Neuropediatrics 37:209–221
3. Baslow MH (2007) N-acetylaspartate and N-acetylaspartylglutamate. In: Lajtha A (ed) Handbook of neurochemistry and molecular neurobiology. Amino Acids and Peptides in the Nervous System, pp 418. 3rd edn, vol 6, Chap. 14. p305-346. Springer Science, NY ISBN:978-0-387-30342-0
4. Moffett JR, Ross B, Arun P et al (2007) N-acetylaspartate in the CNS: from neurodiagnostics to neurobiology. Prog Neurobiol 81:89–131. doi: 10.1016/j.pneurobio.2006.12.003
5. Breitbach-Faller N, Schrader K, Rating D, Wunsch R (2003) Ultrasound findings in follow-up investigations in a case of aspartoacylase deficiency (Canavan disease). Neuropediat 34:96–99. doi: 10.1055/s-2003-39601
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