BIDIRECTIONAL GLENN SHUNT AND REPAIR OF TOTAL ANOMALOUS PULMONARY VENOUS CONNECTION IN A 3 YEARS OLD CHILD WITH HETEROTAXY SYNDROME: A CASE REPORT
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Published:2021-09-30
Issue:3
Volume:54
Page:273-274
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ISSN:2227-9199
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Container-title:Pakistan Heart Journal
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language:
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Short-container-title:Pak Heart J
Author:
Salehi-ardebili Shahyad,Radvar Mohammad,Askari Behnam
Abstract
Right Atrial Isomerism (RAI) and total anomalous pulmonary venous connection (TAPVC) is a rare condition with very high mortality in neonatal period, but outcomes may be better in older children. A cyanotic 3 years old boy with dyspnea and growth retardation diagnosed with RAI and supracardiac type of TAPVC undergone a successful repair of TAPVC and simultaneous Glenn shunt. Older patients with RAI may be a distinct, more suitable group for surgical repair.
Publisher
Pakistan Cardiac Society
Subject
Cardiology and Cardiovascular Medicine