A LARGE SCALP MYXOID NEUROFIBROMA AN UNUSUAL PRESENTATION IN A MIDDLE- AGED PATIENT: A RARE CASE REPORT

Abstract

The transformed cells in a neoplasm, whether benign or malignant, often resemble each other, as though all had been derived from a single progenitor, consistent with the monoclonal origin of the tumor. Myxoid neurobroma (MN) is a benign tumor of perineural origin, which is demonstrated by positive immunohistochemical staining for S100 protein. The most common locations are the face, shoulder, anus, periungual, and feet. To our knowledge, this is the first report of an MN in the scalp, which is a very rare location that has been reported earlier. The differential diagnosis of the tumor at this location MN should be kept in mind. This 56 years old male who presented with a large swelling in the scalp (occipital region) which extended to the nape of nack for last 3 years which is gradually increasing in size along with heaviness, intermittent severe pain in the head. Clinically (25x20) cm size swelling in the occipital area and extending to the nape of the neck. The swelling is nontender. It is ovoid in shape . Soft cystic in consistency, the surface is smooth, margins are well dened, the mobility is absent. Fluctuation test is negative but the swelling is brilliantly transilluminant. CONCLUSION: We report this case because of the rarity of both the tumor and its scalp location and also a giant size and to provide a review of the literature. This case study illustrates that any slowly progressing swelling in an unusual location should have been properly investigated and complete surgical excision is the preferred choice of treatment for future recurrence. The MN should be included in the differential diagnosis of tumors at this location.